Concept information
Preferred term
Phenylalanine Hydroxylase
Definition(s)
- An enzyme of the oxidoreductase class that catalyzes the formation of L-TYROSINE, dihydrobiopterin, and water from L-PHENYLALANINE, tetrahydrobiopterin, and oxygen. Deficiency of this enzyme may cause PHENYLKETONURIAS and PHENYLKETONURIA, MATERNAL. EC 1.14.16.1.
Broader concept(s)
Synonym(s)
- EC 1.14.16.1
- Hydroxylase, Phenylalanine
- L-Phenylalanine,tetrahydrobiopterin:oxygen oxidoreductase (4-hydroxylating)
- Phenylalanine 4 Hydroxylase
- Phenylalanine 4-Hydroxylase
- Phenylalanine 4 Monooxygenase
- Phenylalanine 4-Monooxygenase
Allowable Qualifier(s)
- administration & dosage (Qualifier)
- adverse effects (Qualifier)
- analysis (Qualifier)
- antagonists & inhibitors (Qualifier)
- biosynthesis (Qualifier)
- blood (Qualifier)
- cerebrospinal fluid (Qualifier)
- chemical synthesis (Qualifier)
- chemistry (Qualifier)
- classification (Qualifier)
- deficiency (Qualifier)
- drug effects (Qualifier)
- economics (Qualifier)
- genetics (Qualifier)
- history (Qualifier)
- immunology (Qualifier)
- isolation & purification (Qualifier)
- metabolism (Qualifier)
- pharmacokinetics (Qualifier)
- pharmacology (Qualifier)
- physiology (Qualifier)
- poisoning (Qualifier)
- radiation effects (Qualifier)
- standards (Qualifier)
- supply & distribution (Qualifier)
- therapeutic use (Qualifier)
- toxicity (Qualifier)
- ultrastructure (Qualifier)
- urine (Qualifier)
In other languages
-
French
-
EC 1.14.16.1
-
L-Phenylalanine,tetrahydrobiopterin:oxygen oxidoreductase (4-hydroxylating)
-
Phenylalaninase
-
Phenylalanine 4-hydroxylase
URI
http://data.loterre.fr/ark:/67375/JVR/M0016546
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