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Concept information

Preferred term

Phenylalanine Hydroxylase  

Definition(s)

  • An enzyme of the oxidoreductase class that catalyzes the formation of L-TYROSINE, dihydrobiopterin, and water from L-PHENYLALANINE, tetrahydrobiopterin, and oxygen. Deficiency of this enzyme may cause PHENYLKETONURIAS and PHENYLKETONURIA, MATERNAL. EC 1.14.16.1.

Broader concept(s)

Synonym(s)

  • EC 1.14.16.1
  • Hydroxylase, Phenylalanine
  • L-Phenylalanine,tetrahydrobiopterin:oxygen oxidoreductase (4-hydroxylating)
  • Phenylalanine 4 Hydroxylase
  • Phenylalanine 4-Hydroxylase
  • Phenylalanine 4 Monooxygenase
  • Phenylalanine 4-Monooxygenase

In other languages

  • French

  • EC 1.14.16.1
  • L-Phenylalanine,tetrahydrobiopterin:oxygen oxidoreductase (4-hydroxylating)
  • Phenylalaninase
  • Phenylalanine 4-hydroxylase

URI

http://data.loterre.fr/ark:/67375/JVR/M0016546

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