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Concept information

disease > genetic disease > hereditary disease > ichthyosis linearis circumflexa
... > disease > skin appendages disease > skin disease > dyskeratosis > hyperkeratosis > ichthyosis > ichthyosis linearis circumflexa
disease > skin appendages disease > skin disease > erythroderma > ichthyosis linearis circumflexa

Terme préférentiel

ichthyosis linearis circumflexa  

Définition(s)

  • Ichthyosis linearis circumflexa is a distinctive skin condition of generalized hyperkeratosis and polycyclic and serpiginous erythematous plaques with a characteristic, migratory, double-edged scale at the margins, and is the typical cutaneous manifestation of Netherton's syndrome. (Wikipedia)

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URI

http://data.loterre.fr/ark:/67375/VH8-N3TGF2N9-V

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RDF/XML TURTLE JSON-LD Dernière modif. 14/05/2020